Liver Transplant Image
Polycystic liver is between the white arrows. The polycystic liver has been decompressed. It was even larger before the decompression. The black arrow indicates a normal size liver.
Liver Transplant for PLD From April 12, 2007 New England Journal of Medicine.
A 51-year-old woman with polycystic liver and kidney disease had undergone renal transplantation 21 years before presentation. She had no evidence of cerbrovascular malformations. Both her father and Aunt also had polycystic kidney disease. After the renal transplantation, her liver had become progressively diseased and enlarged through cystic changes. Early satiety, malnutrition, and abdominal pain necessitated a liver transplantation.
The recipient's weight at transplantation was 59 kg. A 9.1-kg liver (white arrow) was removed and replaced with a whole graft that was one tenth the weight of the diseased liver (black arrowhead). A large cyst at the dome of the native liver had to be decompressed (white arrowhead) to allow for access to the recipient's supra hepatic vena cava. She made an excellent recovery and had normal kidney and liver function at 4 years of follow-up.
